CCR2

CC Chemokine Receptor Type 2 (PDB ID: 5T1A) from Homo sapiens 

Created by: John Kanu


CC Chemokine Receptor Type 2 (PDB ID: 5T1A), as found in Homo sapiens, is a transmembrane signaling protein which acts as a chemokine receptor. Chemokine receptors are present in all vertebrate and are part of the superfamily of class A seven-transmembrane guanine nucleotide-binding protein, or G protein-coupled receptors (GPCRs) (1). There are twenty-three known human chemokine receptors, found in human tissue and leukocytes. They are divided into two groups, GCPR receptors and atypical receptors. CCR2 is expressed in its physiological form in monocytes, immature dendritic cells, T-cells, and migrate to the Monocyte Chemoattractant Protein, MCP-1, found in the endogenous CC Chemokine Ligand known as, CCL2 (PDB ID: 2LIE). CCL2 is synthesized within the splenic arteriolar lymphatic sheet and medullary regions of the lymph node and other tumors (2). CCR2 bound to CCL2 and associated ligands are connected to numerous inflammatory and neurodegenerative diseases including atherosclerosis, multiple sclerosis, asthma, neuropathic pain, diabetic nephropathy, as well as cancer. Knowledge of the associations has allowed for studies and trials to develop preventative therapies that target the CCR2-chemokine receptor. Finding the proper drug therapies is done by studying the structure in ternary complexwith orthosteric (BMS-681) (PDB ID: 73R) and allosteric antagonists (CCR2-RA-[R]) (PDB ID: VT5)(1).


Through lipidic cubic phase of the ternary complex (fig. 1) of CCR2, BMS-681, and CCR2-RA-[R]. CCR2 has the capability to form. Other crystals of importance that form are crystals of CXC chemokine receptor type 4 (PDB ID: 30E6, 3O30, 30DU). The secondary structure of CCR2 is comprised of 62% alpha-helices (23 helices, 316 residues), 5% beta-sheets (6 strands; 27 residues), and 33% random coils (165 residues), and contains a single A chain subunit composed of 508 residues (3). It has a molecular weight of 57805.54 Da and an isoelectric point (pI) of 9.30 (4). The central fold of CCR2 contains seven transmembrane alpha-helices connected by three extracellular and intracellular loops (5). The first two extracellular domains and loops do not serve any functional significance. The N-terminal domain is for ligand binding, and the C-terminal domain is towards the cytoplasm. CCR2 shares structural properties that are similar among other chemokine receptors. The extracellular portion is net-negative under normal physiological conditions, while the intracellular portion near the C-terminus has serine and threonine residues that phosphorylate due to Dynamin, a G protein receptor kinase, GRK. Phosphorylation results in the uncoupling of the G protein subunits from the receptor. The phosphorylation and GRK recruit adaptor molecules that link the receptor to a lattice of clathrin that facilitates receptor internalization (6). Ultimately, chemokine receptors are identified by a short N-terminus, a short basic third intracellular domain and a cysteine in each of the three extracellular domains (1).


Additional structural features distinguish CCR2 from other chemokine receptors. CCR2 binds to other important ligands: (2R)-2,3-dihydroxypropyl (9Z)-octadec-9-enoate, zinc ion, and sulfate (1). CCR2 has two important ionic bonds. First, zinc, a metal ion, binds the side chains together. γ-lactam secondary exocyclic amine forms a hydrogen bond with the hydroxyl of His-144,Thr-292, Glu-238, and Glu-1005. There are four prosthetic ligands, VT5 and 73R, and OLC and the Sulfate Ion. (2R)-2,3-dihydroxypropyl (9Z)-octadec-9-enoate contains two active alcohol groups and allows for crystallization. The sulfate ion (SO42-) helps define the substrate-binding site. CCR2 uses the sulfate to bind to the MCP-1 (2). 


The function of the subunit is due to the addition of an orthosteric ligand BMS-681 and allosteric CCR2-RA-[R] antagonist ligand which leads to a site overlap which allows for a highly favorable drug pocket. This drug pocket that is created is highly due to the allosteric CCR2-RA-[R] antagonist. CCR2-RA-[R] is surrounded by a cage using the intracellular ends of helices I-III and VI-VIII. The mixed polarity of CCR2 creates a hydrophobic inner area is surrounded by residuesVal-63, Leu-67, Leu-81, Leu-134, Ala-241, Val-244, Tyr-305, and Phe-312. The outer polar portion of the cage is comprised of Thr-77, Arg-318, Glu-309, Lys-311, and Tyr-315. There is a backbone of residues Arg-237 and Lys-240 (1,2). This binding pock is tightly enclosed and is balanced between hydrophobic and polar, which allows for the site to be highly druggable. The binding bock is created in part of two disulfide bonds, between Cys-32- Cys-277 and Cys-113-Cys-190. CCR2-RA-[R] in its natural form sterically hinders CCR2; therefore, when BMS-681 binding interferes with the chemokine binding site directly and with the GPCR indirectly, forcing an incompatible conformation. Natural receptor-chemokine interactions prove to be challenging for therapy, as the CCR2 has selectivity for multiple ligands which block the ability for a drug pocket (6). Pharmaceutical antagonist and orthosteric ligands inhibit the binding of CCR2 to CCL2, allowing for drug pocket availability (2).


CCR2 shows structural similarities to the Mu-type opioid receptor, lysozyme chimaera(PDB ID: 4DKL) found within Mus musculus. Mu-type opioid receptor is comprised of 70% alpha-helices (20 helices, 326 residues), 4% beta-sheets (8 strands; 28 residues), and 26% random coils (110 residues), and contains a single A chain subunit composed of 464 residues. It has a molecular weight of 55761.68 Da and an isoelectric point (pI) of 9.37 (4,7). Comparisons between the Mu-type opioid receptor and CCR2 resulted in a BLAST E-score of 2.0 x 10-177 (8). An E-score of less than 0.05 indicates that the two proteins have a similar primary structure. The DALI server generated a Z-score of 30.8 (9). A Z-score more significant than 2 indicates that the two proteins are similar among their tertiary structure. The Mu-type opioid receptor binds to six associated ligands. One that is similar to that of CCR2, which is a sulfate ion. The other associated ligands involve: a chloride ion which acts as an ionic bond binding the side chains of the receptor: Ser-261, Glu-270, and Lys-271; [(Z)-octadec-9-enyl] (2R)-2,3-bis(oxidanyl)propanoate, whose role is to act as an intermediate; an antagonist ligand methyl 4-{[(5beta,6alpha)-17-(cyclopropylmethyl)-3,14-dihydroxy-4,5-epoxymorphinan-6-yl]amino}-4-oxobutanoate; a water-soluble, Pentaethylene glycol and cholesterol who modulates the functions of the protein. Mu-type opioid receptor (55761.68 Da) differs from CC Chemokine Receptor 2 (59577.95 Da) by mass, polarity, as well as the multitude (11:4) of extra sulfate ions present. There are also more ligands present in Mu-type opioid receptor than in CC Chemokine Receptor 2 (7).


CCR2 can conform to two similar structures that are not just crystallized versions of itself. First, there is the crystal structure of the CCR4 chemokine receptor in complex with a small molecule antagonist IT1t in I222 space-group (PDB ID: 3OE6). Then there is the crystal structure of CXCR4 and viral chemokine antagonist MIP-II complex (PSI Community Target) (PDB ID: 4RWS) (10). Duchenne muscular dystrophy is the progressive weakness of muscle that is often fatal due to the loss of control of the diaphragm. A dual chemokine receptor, CCR2/CCR5 (PDB ID: 4MBS), treated with 20mg/kg/day of cenicriviroc, an antagonist, can prevent the macrophage accumulation and the progression of the disease (11). CCR2 is a complex receptor protein that can lead to detrimental effects on the human body if not altered with BMS-681 and CCR2-RA-[R].  The effect of the alteration prevents the CCR2 from binding to CCL2, which has the possibility of leading to neuromuscular disease and cancers within the human body (1).